Clinical index

EBV-T/NK-LPDs

(n = 21)

CAEBV

(n = 9)

HV-LPD

(n = 8)

CSEBV + TCL (n = 4)

General information

Sex (Boy: Girl)

4:3

7:2

1:3

3:1

Age of onset > 8 years

12

7

3

2

Manifestation

Fever

17

7

6

4

Lymphadenopathy

11

5

2

4

Hepatomegaly

15

7

4

4

Splenomegaly

14

7

3

4

rash

10

2

8

0

facial swelling

6

1

5

0

Laboratory

examination

Pancytopenia

10

4

4

3

Thrombocytopenia

11

4

4

3

Abnormal liver function

9

4

4

1

Bilirubin disorder

7

2

4

1

LDH increased

11

5

4

2

Coagulation disorders

7

2

3

2

Abnormal renal function

3

2

1

0

Classification

T cell type

16

9

3

4

Complication

HLH

7

3

2

2

Prognosis

Death

16/20 (80%)

6/8 (75%)

6/8 (75%)

4/4 (100%)